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Table 2 Synopsis of recent case reports decribing various phototherapeutic alternatives in a number of sclerotic rarities. [Categories: A – double-blind, randomized, placebo-controlled; B – open, randomised; C – open, non-randomized; D – case series; E – case report]

From: UVA/UVA1 phototherapy and PUVA photochemotherapy in connective tissue diseases and related disorders: a research based review

Disease

Therapy

Dosage

Experience

Comments

Eosinophilic fasciitis

UVA180

low-dose

E

benefit, no valid data available

 

PUVA81

medium-dose

E

 

Pansclerotic morphea

UVA84

low-dose

E

possible efficacy as an adjunct therapy,

 

UVA183

low-dose

E

no valid data available

 

PUVA85,86

medium-dose

E

 

Scleromyxedema

PUVA90–92

high-dose

E

controversial, possible efficacy as an adjunct therapy, no valid data available

Scleredema adultorum Buschke

PUVA95,96

high-dose

E, D

possible therapeutic alternative, cream therapy, no valid data available

POEMS

UVA198

low-dose

E

benefit, no valid data available

Bleomycin-induced scleroderma

UVA199

low-dose

E

limited success, no valid data available

Pansclerotic porphyria cutanea tarda

UVA1101

medium-dose

E

benefit, no valid data available