Skip to main content

Table 1 Median scores in different pemphigus subgroups

From: Estimated cut-off values for pemphigus severity classification according to pemphigus disease area index (PDAI), autoimmune bullous skin disorder intensity score (ABSIS), and anti-desmoglein 1 autoantibodies

Disease site

PDAI

ABSIS

PGA

ABQoL

cutaneous score*

Mucosal score

Total activity score

cutaneous score

Mucosal score**

Total activity score

All patients (IQR)

2 (14)

6 (10)

13 (21.4)

0.1 (3.1)

12.5 (26.5)

15.1 (26)

3.33 (2.83)

31 (15.5)

Cutaneous (IQR)**

13 (12.9)

0

13 (12.9)

3.17 (25.99)

0

3.175 (25.99)

3.16 (4.21)

24.5 (22)

Mucosal (IQR)

0

7 (9.2)

7 (9.2)

0

17.5 (28.88)

17.5 (28.88)

2 (1.58)

36 (5.5)

Mucocutaneous (IQR)

10 (23.8)

6.3 (9)

20 (24.5)

2 .25 (6.76)

15 (25.5)

20.55 (22.86)

4.16 (3)

26 (14)

  1. *Sum of skin and scalp scores for PDAI score
  2. **Sum of scores for oral involvement and severity was considered as mucosal score
  3. Abbreviation: PDAI pemphigus disease area index, ABSIS Autoimmune Bullous Skin Disorder Intensity Score, ABQoL autoimmune bullous disease quality of life, PGA physician global assessment, IQR interquartile range